Abstrakt

Background: Herlyn-Werner-Wunderlich Syndrome or OHVIRA syndrome is uterine didelphys with obstructed hemi-vagina and ipsilateral renal agenesis syndrome is a very rare congenital urogenital anomaly.

Case: A 21-year-old female presented with acute abdomen and severe dysmenorrhea. Ultrasonography performed in obstetric emergency room showed a cystic lesion in right pelvic area, free fluid in Douglas’s pouch and right renal agenesis. Diagnostic laparoscopy revealed uterine didelphys with right ovarian hemi-torsion. A unilateral hysterectomy was conducted.

Conclusion: HWW syndrome could manifest as acute abdominal symptoms and typically requires treatment involving resection of the vaginal septum and drainage of hematometrocolpos.